Revascularization Operation for Moyamoya Disease with Concurrent von Willebrand Disease

Kenji Miki, Koichi Arimura, ataru nishimura, Koji Yoshimoto, Tetsuro Sayama, Koji Iihara

Research output: Contribution to journalArticlepeer-review

1 Citation (Scopus)


Background Although extracranial-intracranial (EC-IC) bypass is an effective treatment strategy for symptomatic moyamoya disease, surgeons need to be cautious regarding the possibility of postoperative hemorrhagic complications in patients with a concurrent coagulation disorder. Here, we describe a case of EC-IC bypass for moyamoya disease concurrent with von Willebrand disease type 1. Case Description Following perioperative replacement of the von Willebrand factor, the patient showed an uneventful and uncomplicated clinical course. Conclusion This is the first reported case of EC-IC bypass being performed for moyamoya disease in a patient with concurrent von Willebrand disease. We emphasize the importance of appropriate management with replacement of the von Willebrand factor during the perioperative period to avoid hemorrhagic complications.

Original languageEnglish
Pages (from-to)991.e17-991.e21
JournalWorld Neurosurgery
Publication statusPublished - Dec 2017

All Science Journal Classification (ASJC) codes

  • Surgery
  • Clinical Neurology


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