Perioperative management of a patient with Bernard-Soulier syndrome that has a refractoriness to platelet transfusion

D. Yoshiga; A. Yoshida; S. Kitahara; C. Harada; Shinichi Ito; Seiji Nakamura; K. Kubo

doi:10.1016/j.ajoms.2011.02.002

Perioperative management of a patient with Bernard-Soulier syndrome that has a refractoriness to platelet transfusion

D. Yoshiga, A. Yoshida, S. Kitahara, C. Harada, Shinichi Ito, Seiji Nakamura, K. Kubo

Maxillofacial Diagnostic & Surgical Sciences

Research output: Contribution to journal › Article › peer-review

2 Citations (Scopus)

Abstract

A patient with Bernard-Soulier syndrome (BSS), characterized by extremely large platelets, thrombocytopenia and prolonged bleeding time underwent general anesthesia for platelet adhesion aberration. This patient has developed a refractoriness to platelet transfusion due to a frequent transfusion of platelets; however the operation was completed without abnormal bleeding by transfusing HLA-matched platelets during the procedure. BSS is a very rare syndrome so there are no well-defined protocols for the management of perioperative bleeding associated with this syndrome. In this report, we present the detail of the perioperative management for these patients with BSS who has a refractoriness to platelet transfusion.

Original language	English
Pages (from-to)	102-104
Number of pages	3
Journal	Asian Journal of Oral and Maxillofacial Surgery
Volume	23
Issue number	2
DOIs	https://doi.org/10.1016/j.ajoms.2011.02.002
Publication status	Published - May 1 2011

All Science Journal Classification (ASJC) codes

Surgery
Oral Surgery
Orthopedics and Sports Medicine

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10.1016/j.ajoms.2011.02.002

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abstract = "A patient with Bernard-Soulier syndrome (BSS), characterized by extremely large platelets, thrombocytopenia and prolonged bleeding time underwent general anesthesia for platelet adhesion aberration. This patient has developed a refractoriness to platelet transfusion due to a frequent transfusion of platelets; however the operation was completed without abnormal bleeding by transfusing HLA-matched platelets during the procedure. BSS is a very rare syndrome so there are no well-defined protocols for the management of perioperative bleeding associated with this syndrome. In this report, we present the detail of the perioperative management for these patients with BSS who has a refractoriness to platelet transfusion.",

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AU - Yoshiga, D.

AU - Yoshida, A.

AU - Kitahara, S.

AU - Harada, C.

AU - Ito, Shinichi

AU - Nakamura, Seiji

AU - Kubo, K.

PY - 2011/5/1

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AB - A patient with Bernard-Soulier syndrome (BSS), characterized by extremely large platelets, thrombocytopenia and prolonged bleeding time underwent general anesthesia for platelet adhesion aberration. This patient has developed a refractoriness to platelet transfusion due to a frequent transfusion of platelets; however the operation was completed without abnormal bleeding by transfusing HLA-matched platelets during the procedure. BSS is a very rare syndrome so there are no well-defined protocols for the management of perioperative bleeding associated with this syndrome. In this report, we present the detail of the perioperative management for these patients with BSS who has a refractoriness to platelet transfusion.

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Perioperative management of a patient with Bernard-Soulier syndrome that has a refractoriness to platelet transfusion

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